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{
    "pk": 1016,
    "title": "Pediatric Innominate Artery Pseudoaneurysm Rupture in Vascular Ehlers-Danlos Syndrome: A Case Report",
    "subtitle": null,
    "abstract": "Introduction:\n Ehlers-Danlos syndrome is a well classified connective tissue disorder recognized by its features of hyperextensibility of joints and hyperelasticity of the skin. However, the rare vascular type (Ehlers-Danlos type IV) is more difficult to identify in the absence, rarity, or subtlety of the classical physical features. Patients presenting to the emergency department (ED) with acute complications of vascular Ehlers-Danlos syndrome may be critically ill, requiring accurate diagnosis and tailored management.\nCase Report:\n This report details a case of spontaneous innominate artery pseudoaneurysm rupture in a pediatric patient with previously undiagnosed Ehlers-Danlos syndrome. Initial ED evaluation was followed by urgent operative intervention and subsequent genetic testing to confirm final diagnosis.\nConclusion:\n Due to its high morbidity and mortality, vascular type Ehlers-Danlos syndrome should be considered in the differential for otherwise unexplained spontaneous vascular injury.",
    "language": "en",
    "license": {
        "name": "Creative Commons Attribution 4.0",
        "short_name": "CC BY 4.0",
        "text": "Attribution — You must give appropriate credit, provide a link to the license, and indicate if changes were made. You may do so in any reasonable manner, but not in any way that suggests the licensor endorses you or your use.\r\n\r\nNo additional restrictions — You may not apply legal terms or technological measures that legally restrict others from doing anything the license permits.",
        "url": "https://creativecommons.org/licenses/by/4.0"
    },
    "keywords": [
        {
            "word": "Pseudoaneurysm"
        },
        {
            "word": "pediatric vascular injury"
        },
        {
            "word": "Ehlers-Danlos syndrome"
        },
        {
            "word": "case report"
        }
    ],
    "section": "Case Reports",
    "is_remote": true,
    "remote_url": "https://escholarship.org/uc/item/2q32s86v",
    "frozenauthors": [
        {
            "first_name": "Aimee",
            "middle_name": "",
            "last_name": "Vos",
            "name_suffix": "",
            "institution": "Advocate Christ Medical Center, Department of Emergency Medicine, Oak Lawn, Illinois",
            "department": "None"
        },
        {
            "first_name": "Katharine",
            "middle_name": "M.",
            "last_name": "Burns",
            "name_suffix": "",
            "institution": "Advocate Christ Medical Center, Department of Emergency Medicine, Oak Lawn, Illinois",
            "department": "None"
        }
    ],
    "date_submitted": "2021-04-24T02:24:09-04:00",
    "date_accepted": "2021-04-24T02:24:09-04:00",
    "date_published": "2021-04-24T02:24:44-04:00",
    "render_galley": null,
    "galleys": [
        {
            "label": "",
            "type": "",
            "path": "https://journalpub.escholarship.org/uciem_cpcem/article/1016/galley/763/download/"
        }
    ]
}